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[1] http:\/\/www.gov.cn\/xinwen\/2018-09\/05\/content_5319392.htm<\/a>锛堣闂棩鏈�2022骞�8鏈�24鏃ワ級<\/p> \n

[2] Anita Hill, et al. The Incidence and Prevalence of Paroxysmal Nocturnal Hemoglobinuria (PNH) and Survival of Patients in Yorkshire. Blood 2006;108 (11): 985.<\/p> \n

[3] 缃曡鐥呰瘖鐤楁寚鍗楋紙2019骞寸増锛�: 547-551<\/p> \n

[4] Hillmen P锛宔t al. N Engl J Med 1995锛�333:1253-1258.<\/p> \n

[5] 鍒樺皬鑽o紝娌堥锛屾▕鍓戦攱锛岀瓑. 涓浗鍎跨闈炲吀鍨嬫憾琛€灏挎瘨缁煎悎寰佽瘖娌昏鑼冧笓瀹跺叡璇哰J]. 涓浗瀹炵敤鍎跨鏉傚織, DOI:<\/p> \n

[6] Afshar-Kharghan V.Hematology Am Soc Hematol Educ Program. 2016; 2016(1):217-225<\/p> \n

[7] https:\/\/alexion.com\/en\/our-medicines\/medicines\/soliris#<\/a> 锛堣闂棩鏈燂細2022骞�8鏈�24鏃ワ級<\/p> \n

[8] Hillmen P, et al. Blood. 2007 Dec 1<\/span>;110(12):4123-8<\/p> \n

[9] Legendre CM, et al. N Engl J Med. 2013 Jun 6<\/span>;368(23):2169-81.<\/p> \n

[10] Hillmen P, et al. British Journal of Haematology, 2013, 162, 62鈥�73.<\/p> \n

[11] Legendre, C.M. et al. N Engl J Med 2013; 368:2169-2181.<\/p>"]; $("#dvExtra").html(content_array[0]);})();